ICD-10 Code D56.4 | Hereditary persistence of fetal hemoglobin [HPFH] Symptoms, Diagnosis, Billing

Hereditary persistence of fetal hemoglobin (HPFH) is a genetic condition characterized by the continued production of fetal hemoglobin (HbF) into adulthood. This condition is caused by mutations in the regulatory genes that control hemoglobin production. Clinically, HPFH is significant as it can lead to a mild form of anemia or provide a protective effect against sickle cell disease and beta-thalassemia. The ICD-10 Code D56.4 facilitates accurate diagnosis, documentation, medical billing, and public health reporting for this condition.

What is ICD-10 Code D56.4 for Hereditary persistence of fetal hemoglobin [HPFH]?

ICD-10 Code D56.4 represents Hereditary persistence of fetal hemoglobin (HPFH), a condition where individuals continue to produce fetal hemoglobin beyond the typical perinatal period. This condition is often benign but can be associated with mild anemia. The code should be used in clinical documentation and billing when diagnosing patients with HPFH, ensuring proper identification of the condition for treatment and management.

ICD-10 Code D56.4 – Clinical Definition and Explanation of Hereditary persistence of fetal hemoglobin [HPFH]

Hereditary persistence of fetal hemoglobin (HPFH) is primarily caused by genetic mutations that affect the regulation of hemoglobin production, leading to elevated levels of fetal hemoglobin in adults. This condition is generally asymptomatic but may require medical attention if anemia develops. Understanding HPFH is crucial for appropriate management and genetic counseling.

Key Clinical Features:

• Elevated fetal hemoglobin levels in adults
• Mild anemia in some cases
• Genetic inheritance patterns (autosomal dominant or recessive)
• Potential protective effects against certain hemoglobinopathies

ICD-10 Code D56.4 for Hereditary persistence of fetal hemoglobin [HPFH] – SOAP Notes & Clinical Use

ICD-10 Code D56.4 is utilized in SOAP notes to document the presence of hereditary persistence of fetal hemoglobin (HPFH). It aids in capturing patient symptoms, assessments, and treatment plans, ensuring comprehensive care in both acute and chronic settings.

What Does ICD-10 Code D56.4 for Hereditary persistence of fetal hemoglobin [HPFH] Mean in SOAP Notes?

In SOAP notes, ICD-10 Code D56.4 connects subjective patient reports and objective clinical findings to a formal diagnosis of HPFH. This code is essential for ensuring continuity of care, supporting accurate billing, and meeting EHR documentation standards.

Treatment Options for ICD-10 Code D56.4 – Hereditary persistence of fetal hemoglobin [HPFH]

Management of hereditary persistence of fetal hemoglobin (HPFH) typically focuses on monitoring and supportive care, as the condition is often asymptomatic. In cases where anemia is present, treatment may be necessary.

Antibiotic Therapy:

Supportive Care:

• Regular monitoring of hemoglobin levels
• Nutritional support to prevent anemia
• Genetic counseling for affected families

Infection Control:

How to Document Symptoms of Hereditary persistence of fetal hemoglobin [HPFH] (ICD-10 D56.4) in SOAP Notes

Subjective:

• Patient reports fatigue and mild weakness.
• Family history of hemoglobin disorders.
• No history of significant bleeding or transfusions.

Objective:

• Hemoglobin level: 11.5 g/dL.
• Elevated fetal hemoglobin percentage: 15%.
• No splenomegaly or other physical exam findings.

Secure, compliant, and built for trust

HIPAA-compliant and designed with privacy in mind, your patient’s data is protected. Focus on care while we safeguard your information.

Learn more

SOAP Note Guidelines for Diagnosing Hereditary persistence of fetal hemoglobin [HPFH] (ICD-10 Code D56.4)

Assessment:

• Diagnosis: Hereditary persistence of fetal hemoglobin (HPFH), mild anemia.
• ICD-10 Code: D56.4.
• Contributing factors: Genetic predisposition.

Plan:

• Monitor hemoglobin levels regularly.
• Provide education on the condition and its implications.
• Consider genetic counseling for family members.

Treatment & Plan Section for ICD-10 Code D56.4 – Hereditary persistence of fetal hemoglobin [HPFH]

• Monitor hemoglobin levels and assess for anemia.
• Educate patients on lifestyle modifications to support overall health.
• Encourage regular follow-up appointments for ongoing assessment.
• Consider referral to a hematologist if complications arise.

Using ICD-10 Code D56.4 for Hereditary persistence of fetal hemoglobin [HPFH] in Billing & SOAP Note Compliance

• Ensure accurate documentation of symptoms and clinical findings in SOAP notes.
• Use the code in appropriate clinical settings, including outpatient and inpatient care.
• Align treatment plans with clinical guidelines to support justified billing.
• Document any related conditions or complications to enhance coding accuracy.

Related ICD-10 Codes Often Used with Hereditary persistence of fetal hemoglobin [HPFH]

• D56.0 – Sickle-cell disease with crisis
• D56.1 – Sickle-cell disease without crisis
• D56.2 – Sickle-cell trait
• D56.3 – Beta-thalassemia

ICD-10 Code D56.4 in Medical Billing and Insurance for Hereditary persistence of fetal hemoglobin [HPFH]

ICD-10 Code D56.4 is crucial for billing purposes, particularly in hospital, emergency room, or outpatient settings where HPFH is diagnosed or managed.

Billing Notes:

• Document all relevant clinical findings to support the use of D56.4.
• Use the code in conjunction with other relevant diagnoses for comprehensive billing.
• Ensure that the patient's medical history reflects the condition for accurate claims processing.

Common CPT Pairings: